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How strict is galactose restriction in adults with galactosaemia?: international practice

Dietary management of 418 adult patients with galactosaemia (from 39 centres/12 countries) was compared. All centres advised lactose restriction, 6 restricted galactose from galactosides ± fruits and vegetables and 12 offal. 38% (n = 15) relaxed diet by: 1) allowing traces of lactose in manufactured...

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Hauptverfasser: Adam, Sarah (VerfasserIn) , Sahm, Katja (VerfasserIn)
Dokumenttyp: Article (Journal)
Sprache:Englisch
Veröffentlicht: 7 April 2015
In: Molecular genetics and metabolism
Year: 2015, Jahrgang: 115, Heft: 1, Pages: 23-26
ISSN:1096-7206
DOI:10.1016/j.ymgme.2015.03.008
Online-Zugang:Verlag, Volltext: http://dx.doi.org/10.1016/j.ymgme.2015.03.008
Verlag, Volltext: http://www.sciencedirect.com/science/article/pii/S1096719215000888
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Verfasserangaben:S. Adam, R. Akroyd, S. Bernabei, S. Bollhalder, S. Boocock, A. Burlina, T. Coote, K. Corthouts, J. Dalmau, S. Dawson, S. Defourny, A. De Meyer, A. Desloovere, Y. Devlin, M. Diels, K. Dokoupil, S. Donald, S. Evans, I. Fasan, C. Ferguson, S. Ford, M. Forga, G. Gallo, S.C. Grünert, M. Heddrich-Ellerbrok, C. Heidenborg, C. Jonkers, K. Lefebure, K. Luyten, A. MacDonald, U. Meyer, A. Micciche, E. Müller, P. Portnoi, S. Ripley, M. Robert, L.V. Robertson, S. Rosenbaum-Fabian, K. Sahm, S. Schultz, K. Singleton, E. Sjöqvist, L. Stoelen, A. Terry, S. Thompson, C. Timmer, K. Vande Kerckhove, L. van der Ploeg, M. Van Driessche, M. van Rijn, A. van Teeffelen-Heithoff, I. Vitoria, C. Voillot, J. Wenz, M. Westbrook, J. Wildgoose, H. Zweers

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