Pleuroparenchymal fibroelastosis in association with carcinomas

PPFE is a rare disease characterized by upper lobe pleural fibrosis and parenchymal fibroelastosis. Its aetiology is considered idiopathic, although possible causative factors have been described. An association of PPFE with solid tumours is unknown and has not been considered previously. We identif...

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Hauptverfasser: Baroke, Eva (VerfasserIn) , Heußel, Claus Peter (VerfasserIn) , Warth, Arne (VerfasserIn) , Eichinger, Monika (VerfasserIn) , Oltmanns, Ute (VerfasserIn) , Palmowski, Karin (VerfasserIn) , Herth, Felix (VerfasserIn) , Kreuter, Michael (VerfasserIn)
Dokumenttyp: Article (Journal)
Sprache:Englisch
Veröffentlicht: 2016
In: Respirology
Year: 2016, Jahrgang: 21, Heft: 1, Pages: 191-194
ISSN:1440-1843
DOI:10.1111/resp.12654
Online-Zugang:Verlag, lizenzpflichtig, Volltext: https://doi.org/10.1111/resp.12654
Verlag, lizenzpflichtig, Volltext: https://onlinelibrary.wiley.com/doi/abs/10.1111/resp.12654
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Verfasserangaben:Eva Baroke, Claus Peter Heussel, Arne Warth, Monika Eichinger, Ute Oltmanns, Karin Palmowski, Felix J. F. Herth and Michael Kreuter
Beschreibung
Zusammenfassung:PPFE is a rare disease characterized by upper lobe pleural fibrosis and parenchymal fibroelastosis. Its aetiology is considered idiopathic, although possible causative factors have been described. An association of PPFE with solid tumours is unknown and has not been considered previously. We identified six patients with PPFE, four of them with a coexisting malignancy. The case series suggests that PPFE might be an implication of varying factors rather than being an exclusively idiopathic condition.
Beschreibung:First published: 13 October 2015
Gesehen am 30.07.2020
Beschreibung:Online Resource
ISSN:1440-1843
DOI:10.1111/resp.12654