Clinical, paraclinical and serological findings in Susac syndrome: an international multicenter study

Susac syndrome (SuS) is a rare disorder thought to be caused by autoimmune-mediated occlusions of microvessels in the brain, retina and inner ear leading to central nervous system (CNS) dysfunction, visual disturbances due to branch retinal artery occlusions (BRAO), and hearing deficits. Recently, a...

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Hauptverfasser: Jarius, Sven (VerfasserIn) , Kleffner, Ilka Anna Elisabeth (VerfasserIn) , Dörr, Jan-Markus (VerfasserIn) , Sastre-Garriga, Jaume (VerfasserIn) , Illes, Zsolt (VerfasserIn) , Eggenberger, Eric (VerfasserIn) , Chalk, Colin (VerfasserIn) , Ringelstein, Marius (VerfasserIn) , Aktaş, Orhan (VerfasserIn) , Montalbán, Xavier (VerfasserIn) , Fechner, Kai (VerfasserIn) , Stöcker, Winfried (VerfasserIn) , Ringelstein, Erich B. (VerfasserIn) , Paul, Friedemann (VerfasserIn) , Wildemann, Brigitte (VerfasserIn)
Dokumenttyp: Article (Journal)
Sprache:Englisch
Veröffentlicht: 08 March 2014
In: Journal of neuroinflammation
Year: 2014, Jahrgang: 11
ISSN:1742-2094
DOI:10.1186/1742-2094-11-46
Online-Zugang:Verlag, lizenzpflichtig, Volltext: https://doi.org/10.1186/1742-2094-11-46
Volltext
Verfasserangaben:Sven Jarius, Ilka Kleffner, Jan M. Dörr, Jaume Sastre-Garriga, Zsolt Illes, Eric Eggenberger, Colin Chalk, Marius Ringelstein, Orhan Aktas, Xavier Montalban, Kai Fechner, Winfried Stöcker, Erich B. Ringelstein, Friedemann Paul and Brigitte Wildemann
Beschreibung
Zusammenfassung:Susac syndrome (SuS) is a rare disorder thought to be caused by autoimmune-mediated occlusions of microvessels in the brain, retina and inner ear leading to central nervous system (CNS) dysfunction, visual disturbances due to branch retinal artery occlusions (BRAO), and hearing deficits. Recently, a role for anti-endothelial cell antibodies (AECA) in SuS has been proposed.
Beschreibung:Gesehen am 06.08.2020
Beschreibung:Online Resource
ISSN:1742-2094
DOI:10.1186/1742-2094-11-46