Clinical, paraclinical and serological findings in Susac syndrome: an international multicenter study

Susac syndrome (SuS) is a rare disorder thought to be caused by autoimmune-mediated occlusions of microvessels in the brain, retina and inner ear leading to central nervous system (CNS) dysfunction, visual disturbances due to branch retinal artery occlusions (BRAO), and hearing deficits. Recently, a...

Ausführliche Beschreibung

Gespeichert in:
Bibliographische Detailangaben
Hauptverfasser: Jarius, Sven (VerfasserIn) , Kleffner, Ilka Anna Elisabeth (VerfasserIn) , Dörr, Jan-Markus (VerfasserIn) , Sastre-Garriga, Jaume (VerfasserIn) , Illes, Zsolt (VerfasserIn) , Eggenberger, Eric (VerfasserIn) , Chalk, Colin (VerfasserIn) , Ringelstein, Marius (VerfasserIn) , Aktaş, Orhan (VerfasserIn) , Montalbán, Xavier (VerfasserIn) , Fechner, Kai (VerfasserIn) , Stöcker, Winfried (VerfasserIn) , Ringelstein, Erich B. (VerfasserIn) , Paul, Friedemann (VerfasserIn) , Wildemann, Brigitte (VerfasserIn)
Dokumenttyp: Article (Journal)
Sprache:Englisch
Veröffentlicht: 08 March 2014
In: Journal of neuroinflammation
Year: 2014, Jahrgang: 11
ISSN:1742-2094
DOI:10.1186/1742-2094-11-46
Online-Zugang:Verlag, lizenzpflichtig, Volltext: https://doi.org/10.1186/1742-2094-11-46
Volltext
Verfasserangaben:Sven Jarius, Ilka Kleffner, Jan M. Dörr, Jaume Sastre-Garriga, Zsolt Illes, Eric Eggenberger, Colin Chalk, Marius Ringelstein, Orhan Aktas, Xavier Montalban, Kai Fechner, Winfried Stöcker, Erich B. Ringelstein, Friedemann Paul and Brigitte Wildemann

MARC

LEADER 00000caa a2200000 c 4500
001 1726538893
003 DE-627
005 20220818170609.0
007 cr uuu---uuuuu
008 200806s2014 xx |||||o 00| ||eng c
024 7 |a 10.1186/1742-2094-11-46  |2 doi 
035 |a (DE-627)1726538893 
035 |a (DE-599)KXP1726538893 
035 |a (OCoLC)1341352108 
040 |a DE-627  |b ger  |c DE-627  |e rda 
041 |a eng 
084 |a 33  |2 sdnb 
100 1 |a Jarius, Sven  |e VerfasserIn  |0 (DE-588)1054615918  |0 (DE-627)791654818  |0 (DE-576)410367478  |4 aut 
245 1 0 |a Clinical, paraclinical and serological findings in Susac syndrome  |b an international multicenter study  |c Sven Jarius, Ilka Kleffner, Jan M. Dörr, Jaume Sastre-Garriga, Zsolt Illes, Eric Eggenberger, Colin Chalk, Marius Ringelstein, Orhan Aktas, Xavier Montalban, Kai Fechner, Winfried Stöcker, Erich B. Ringelstein, Friedemann Paul and Brigitte Wildemann 
264 1 |c 08 March 2014 
300 |a 11 
336 |a Text  |b txt  |2 rdacontent 
337 |a Computermedien  |b c  |2 rdamedia 
338 |a Online-Ressource  |b cr  |2 rdacarrier 
500 |a Gesehen am 06.08.2020 
520 |a Susac syndrome (SuS) is a rare disorder thought to be caused by autoimmune-mediated occlusions of microvessels in the brain, retina and inner ear leading to central nervous system (CNS) dysfunction, visual disturbances due to branch retinal artery occlusions (BRAO), and hearing deficits. Recently, a role for anti-endothelial cell antibodies (AECA) in SuS has been proposed. 
700 1 |a Kleffner, Ilka Anna Elisabeth  |d 1977-  |e VerfasserIn  |0 (DE-588)129402834  |0 (DE-627)394712293  |0 (DE-576)297642464  |4 aut 
700 1 |a Dörr, Jan-Markus  |d 1974-  |e VerfasserIn  |0 (DE-588)124900259  |0 (DE-627)367769603  |0 (DE-576)294558810  |4 aut 
700 1 |a Sastre-Garriga, Jaume  |e VerfasserIn  |4 aut 
700 1 |a Illes, Zsolt  |e VerfasserIn  |4 aut 
700 1 |a Eggenberger, Eric  |e VerfasserIn  |4 aut 
700 1 |a Chalk, Colin  |e VerfasserIn  |4 aut 
700 1 |a Ringelstein, Marius  |d 1977-  |e VerfasserIn  |0 (DE-588)136773559  |0 (DE-627)694645745  |0 (DE-576)301269084  |4 aut 
700 1 |a Aktaş, Orhan  |d 1972-  |e VerfasserIn  |0 (DE-588)122636112  |0 (DE-627)08206105X  |0 (DE-576)251076679  |4 aut 
700 1 |a Montalbán, Xavier  |e VerfasserIn  |0 (DE-588)138153868  |0 (DE-627)599897120  |0 (DE-576)306589079  |4 aut 
700 1 |a Fechner, Kai  |e VerfasserIn  |4 aut 
700 1 |a Stöcker, Winfried  |d 1947-  |e VerfasserIn  |0 (DE-588)115068707X  |0 (DE-627)1010885987  |0 (DE-576)497185520  |4 aut 
700 1 |a Ringelstein, Erich B.  |d 1948-  |e VerfasserIn  |0 (DE-588)130361402  |0 (DE-627)500079358  |0 (DE-576)170024091  |4 aut 
700 1 |a Paul, Friedemann  |d 1967-  |e VerfasserIn  |0 (DE-588)120885476  |0 (DE-627)080947700  |0 (DE-576)292431309  |4 aut 
700 1 |a Wildemann, Brigitte  |e VerfasserIn  |0 (DE-588)110203844  |0 (DE-627)510150004  |0 (DE-576)171831330  |4 aut 
773 0 8 |i Enthalten in  |t Journal of neuroinflammation  |d London : BioMed Central, 2004  |g 11(2014) Artikel-Nummer 46, 11 Seiten  |h Online-Ressource  |w (DE-627)391784781  |w (DE-600)2156455-3  |w (DE-576)12192985X  |x 1742-2094  |7 nnas  |a Clinical, paraclinical and serological findings in Susac syndrome an international multicenter study 
773 1 8 |g volume:11  |g year:2014  |g extent:11  |a Clinical, paraclinical and serological findings in Susac syndrome an international multicenter study 
856 4 0 |u https://doi.org/10.1186/1742-2094-11-46  |x Verlag  |x Resolving-System  |z lizenzpflichtig  |3 Volltext 
951 |a AR 
992 |a 20200806 
993 |a Article 
994 |a 2014 
998 |g 110203844  |a Wildemann, Brigitte  |m 110203844:Wildemann, Brigitte  |d 910000  |d 911100  |e 910000PW110203844  |e 911100PW110203844  |k 0/910000/  |k 1/910000/911100/  |p 15  |y j 
998 |g 1054615918  |a Jarius, Sven  |m 1054615918:Jarius, Sven  |d 910000  |d 911100  |e 910000PJ1054615918  |e 911100PJ1054615918  |k 0/910000/  |k 1/910000/911100/  |p 1  |x j 
999 |a KXP-PPN1726538893  |e 3735942423 
BIB |a Y 
SER |a journal 
JSO |a {"id":{"eki":["1726538893"],"doi":["10.1186/1742-2094-11-46"]},"physDesc":[{"extent":"11 S."}],"note":["Gesehen am 06.08.2020"],"recId":"1726538893","type":{"media":"Online-Ressource","bibl":"article-journal"},"relHost":[{"disp":"Clinical, paraclinical and serological findings in Susac syndrome an international multicenter studyJournal of neuroinflammation","part":{"year":"2014","volume":"11","text":"11(2014) Artikel-Nummer 46, 11 Seiten","extent":"11"},"recId":"391784781","id":{"issn":["1742-2094"],"eki":["391784781"],"zdb":["2156455-3"]},"type":{"media":"Online-Ressource","bibl":"periodical"},"physDesc":[{"extent":"Online-Ressource"}],"pubHistory":["1.2004 -"],"origin":[{"dateIssuedKey":"2004","publisherPlace":"London","dateIssuedDisp":"2004-","publisher":"BioMed Central"}],"language":["eng"],"titleAlt":[{"title":"JNI"}],"note":["Gesehen am 12.07.10"],"title":[{"title":"Journal of neuroinflammation","subtitle":"JNI","title_sort":"Journal of neuroinflammation"}]}],"person":[{"display":"Jarius, Sven","family":"Jarius","given":"Sven","role":"aut","roleDisplay":"VerfasserIn"},{"roleDisplay":"VerfasserIn","role":"aut","given":"Ilka Anna Elisabeth","family":"Kleffner","display":"Kleffner, Ilka Anna Elisabeth"},{"display":"Dörr, Jan-Markus","given":"Jan-Markus","family":"Dörr","role":"aut","roleDisplay":"VerfasserIn"},{"display":"Sastre-Garriga, Jaume","family":"Sastre-Garriga","given":"Jaume","role":"aut","roleDisplay":"VerfasserIn"},{"roleDisplay":"VerfasserIn","role":"aut","family":"Illes","given":"Zsolt","display":"Illes, Zsolt"},{"given":"Eric","family":"Eggenberger","display":"Eggenberger, Eric","roleDisplay":"VerfasserIn","role":"aut"},{"role":"aut","roleDisplay":"VerfasserIn","display":"Chalk, Colin","given":"Colin","family":"Chalk"},{"given":"Marius","family":"Ringelstein","display":"Ringelstein, Marius","roleDisplay":"VerfasserIn","role":"aut"},{"display":"Aktaş, Orhan","family":"Aktaş","given":"Orhan","role":"aut","roleDisplay":"VerfasserIn"},{"roleDisplay":"VerfasserIn","role":"aut","family":"Montalbán","given":"Xavier","display":"Montalbán, Xavier"},{"display":"Fechner, Kai","given":"Kai","family":"Fechner","role":"aut","roleDisplay":"VerfasserIn"},{"display":"Stöcker, Winfried","given":"Winfried","family":"Stöcker","role":"aut","roleDisplay":"VerfasserIn"},{"display":"Ringelstein, Erich B.","family":"Ringelstein","given":"Erich B.","role":"aut","roleDisplay":"VerfasserIn"},{"family":"Paul","given":"Friedemann","display":"Paul, Friedemann","roleDisplay":"VerfasserIn","role":"aut"},{"display":"Wildemann, Brigitte","given":"Brigitte","family":"Wildemann","role":"aut","roleDisplay":"VerfasserIn"}],"name":{"displayForm":["Sven Jarius, Ilka Kleffner, Jan M. Dörr, Jaume Sastre-Garriga, Zsolt Illes, Eric Eggenberger, Colin Chalk, Marius Ringelstein, Orhan Aktas, Xavier Montalban, Kai Fechner, Winfried Stöcker, Erich B. Ringelstein, Friedemann Paul and Brigitte Wildemann"]},"language":["eng"],"origin":[{"dateIssuedKey":"2014","dateIssuedDisp":"08 March 2014"}],"title":[{"title_sort":"Clinical, paraclinical and serological findings in Susac syndrome","subtitle":"an international multicenter study","title":"Clinical, paraclinical and serological findings in Susac syndrome"}]} 
SRT |a JARIUSSVENCLINICALPA0820