Evaluation of right ventricular function in patients with propionic acidemia: a cross-sectional study
In propionic acidemia (PA), myocardial involvement often leads to progressive cardiac dysfunction of the left ventricle (LV). Cardiomyopathy (CM) is an important contributor to mortality. Although known to be of prognostic value in CM, there are no published data on right ventricular (RV) function i...
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| Hauptverfasser: | , , , , , , , |
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| Dokumenttyp: | Article (Journal) |
| Sprache: | Englisch |
| Veröffentlicht: |
5 January 2023
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| In: |
Children
Year: 2023, Jahrgang: 10, Heft: 1, Pages: 1-13 |
| ISSN: | 2227-9067 |
| DOI: | 10.3390/children10010113 |
| Online-Zugang: | Verlag, kostenfrei, Volltext: https://doi.org/10.3390/children10010113 Verlag, kostenfrei, Volltext: https://www.mdpi.com/2227-9067/10/1/113 
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| Verfasserangaben: | Alexander Kovacevic, Sven F. Garbade, Friederike Hörster, Georg F. Hoffmann, Matthias Gorenflo, Derliz Mereles, Stefan Kölker and Christian Staufner |
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| 520 | |a In propionic acidemia (PA), myocardial involvement often leads to progressive cardiac dysfunction of the left ventricle (LV). Cardiomyopathy (CM) is an important contributor to mortality. Although known to be of prognostic value in CM, there are no published data on right ventricular (RV) function in PA patients. | ||
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