A follicular dendritic cell sarcoma of the mediastinum with immature T cells and association with myasthenia gravis
Follicular dendritic cell (FDC) sarcoma is a very rare neoplasm showing morphologic and phenotypic features of FDCs. It occurs primarily in lymph nodes but also in extranodal sites. So far, there have been no reports on FDC sarcoma associated with myasthenia gravis. In the following we will present...
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| Autori principali: | , , , , , |
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| Natura: | Article (Journal) |
| Lingua: | inglese |
| Pubblicazione: |
[May 2010]
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| In: |
The American journal of surgical pathology
Year: 2010, Volume: 34, Fascicolo: 5, Pages: 742-745 |
| ISSN: | 1532-0979 |
| DOI: | 10.1097/PAS.0b013e3181d7a2ee |
| Accesso online: | Verlag, lizenzpflichtig, Volltext: https://doi.org/10.1097/PAS.0b013e3181d7a2ee Verlag, lizenzpflichtig, Volltext: https://journals.lww.com/ajsp/Fulltext/2010/05000/A_Follicular_Dendritic_Cell_Sarcoma_of_the.20.aspx 
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| Note sull'autore: | Marc Hartert, Philipp Ströbel, Manfred Dahm, Wilfred Nix, Alexander Marx, and Christian-Friedrich Vahl |
| Riassunto: | Follicular dendritic cell (FDC) sarcoma is a very rare neoplasm showing morphologic and phenotypic features of FDCs. It occurs primarily in lymph nodes but also in extranodal sites. So far, there have been no reports on FDC sarcoma associated with myasthenia gravis. In the following we will present a case of an FDC tumor of the mediastinum associated with paraneoplastic myasthenia gravis in a 39-year-old man. The tumor contained a major proportion of immature T cells, which may be connected to this patient's very unusual clinical presentation with autoimmune phenomena. Extranodal FDC sarcomas still seem hardly noticed, and their clinical and pathologic characteristics remain to be better defined. |
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| Descrizione del documento: | Gesehen am 24.03.2023 |
| Descrizione fisica: | Online Resource |
| ISSN: | 1532-0979 |
| DOI: | 10.1097/PAS.0b013e3181d7a2ee |