Erythrokeratolysis hiemalis: scaling erythematous genodermatosis with seasonal manifestation
Erythrokeratolysis hiemalis, keratolytic winter erythema or Oudtshoorn skin has been reported from the South African district of Oudtshoorn as a dominantly inherited dermatosis beginning in early childhood, in some cases with circinar scaling erythemas. Seasonal manifestation in winter-time and a ch...
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| Hauptverfasser: | , , , , |
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| Dokumenttyp: | Article (Journal) |
| Sprache: | Englisch |
| Veröffentlicht: |
1994
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| In: |
Der Hautarzt
Year: 1994, Jahrgang: 45, Heft: 11, Pages: 776-779 |
| ISSN: | 1432-1173 |
| DOI: | 10.1007/s001050050170 |
| Online-Zugang: | Verlag, lizenzpflichtig, Volltext: https://doi.org/10.1007/s001050050170
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| Verfasserangaben: | Dieter Krahl, Andrea Sigwart, Wolfgang Hartschuh, Ingrun Anton-Lamprecht, Detlef Petzoldt |
| Zusammenfassung: | Erythrokeratolysis hiemalis, keratolytic winter erythema or Oudtshoorn skin has been reported from the South African district of Oudtshoorn as a dominantly inherited dermatosis beginning in early childhood, in some cases with circinar scaling erythemas. Seasonal manifestation in winter-time and a characteristic multiform histology distinguish this dermatosis from other childhood scaling erythemas. We present clinical, histological and preliminary immunohistological data of a 4-year-old girl with the attributes of erythrokeratolysis hiemalis. No ancestors from the endemic region were traced. The lack of further cases in the family is interpreted as indicative of a spontaneous dominant new mutation. |
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| Beschreibung: | Gesehen am 04.10.2023 |
| Beschreibung: | Online Resource |
| ISSN: | 1432-1173 |
| DOI: | 10.1007/s001050050170 |