The frequency of non-motor symptoms in SCA3 and their association with disease severity and lifestyle factors

Non-motor symptoms (NMS) are a substantial burden for patients with SCA3. There are limited data on their frequency, and their relation with disease severity and activities of daily living is not clear. In addition, lifestyle may either influence or be affected by the occurrence of NMS.

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Main Authors: Hengel, Holger (Author) , Martus, Peter (Author) , Faber, Jennifer (Author) , Giunti, Paola (Author) , Garcia-Moreno, Hector (Author) , Solanky, Nita (Author) , Klockgether, Thomas (Author) , Reetz, Kathrin (Author) , van de Warrenburg, Bart P. (Author) , Santana, Magda M. (Author) , Silva, Patrick (Author) , Cunha, Inês (Author) , de Almeida, Luís Pereira (Author) , Timmann-Braun, Dagmar (Author) , Infante, Jon (Author) , de Vries, Jeroen (Author) , Lima, Manuela (Author) , Pires, Paula (Author) , Bushara, Khalaf (Author) , Jacobi, Heike (Author) , Onyike, Chiadi (Author) , Schmahmann, Jeremy D. (Author) , Hübener-Schmid, Jeannette (Author) , Synofzik, Matthis (Author) , Schöls, Ludger (Author)
Corporate Author: European Spinocerebellar Ataxia Type-3/Machado-Joseph Disease Initiative (ESMI) Study Group (Author)
Format: Article (Journal)
Language:English
Published: 2 November 2022
In: Journal of neurology
Year: 2023, Volume: 270, Issue: 2, Pages: 944-952
ISSN:1432-1459
DOI:10.1007/s00415-022-11441-z
Online Access:Resolving-System, kostenfrei, Volltext: https://doi.org/10.1007/s00415-022-11441-z
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Author Notes:Holger Hengel, Peter Martus, Jennifer Faber, Paola Giunit, Hector Garcia-Moreno, Nita Solanky, Thomas Klockgether, Kathrin Reetz, Bart P. van de Warrenburg, Magda M. Santana, Patrick Silva, Inês Cunha, Luís Pereira de Almeida, Dagmar Timmann, Jon Infante, Jeroen de Vries, Manuela Lima, Paula Pires, Khalaf Bushara, Heike Jacobi, Chiadi Onyike, Jeremy D. Schmahmann, Jeannette Hübener-Schmid, Matthis Synofzik, European Spinocerebellar Ataxia Type-3/Machado-Joseph Disease Initiative (ESMI) Study Group, Ludger Schöls

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