Growth dynamics of transversal body dimensions and proportions, with related clinical determinants in children with X-linked hypophosphatemia treated with phosphate supplements and active vitamin D

Children with X-linked hypophosphatemia (XLH) present with rickets, leg deformities, and growth failure. Bone stability depends on balanced bone growth in both length and width. Data on body proportions, including transverse body dimensions, in children with XLH treated with phosphate supplements an...

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Hauptverfasser: Brieger, Laura Celine (VerfasserIn) , Przygodda, Stephan (VerfasserIn) , Bohlen, Alina Verena (VerfasserIn) , Rehberg, Mirko (VerfasserIn) , Konrad, Martin (VerfasserIn) , Schlingmann, Karl Peter (VerfasserIn) , Hiort, Olaf (VerfasserIn) , Schmidt, Dorothee (VerfasserIn) , John-Kroegel, Ulrike (VerfasserIn) , Wühl, Elke (VerfasserIn) , Kemper, Markus J. (VerfasserIn) , Derichs, Ute (VerfasserIn) , Patzer, Ludwig (VerfasserIn) , Albers, Norbert (VerfasserIn) , Dunstheimer, Désirée Patricia Alexandra (VerfasserIn) , Heger, Sabine (VerfasserIn) , Grohmann-Held, Karina (VerfasserIn) , Schroeder, Carmen (VerfasserIn) , Jorch, Norbert (VerfasserIn) , Schmid, Elmar (VerfasserIn) , Staude, Hagen (VerfasserIn) , Weitz, Marcus (VerfasserIn) , Freiberg, Clemens (VerfasserIn) , Huebner, Angela (VerfasserIn) , Heitmeyer-Pyper, Anke (VerfasserIn) , Spartà, Giuseppina (VerfasserIn) , Partsch, Carl-Joachim (VerfasserIn) , Marx, Michaela (VerfasserIn) , Land, Christof (VerfasserIn) , Baus, Inka (VerfasserIn) , Wilkening, Frauke (VerfasserIn) , Moeller, Kristina (VerfasserIn) , Simic-Schleicher, Gunter (VerfasserIn) , Empting, Susann (VerfasserIn) , Metzing, Oliver (VerfasserIn) , Wagner, Verena (VerfasserIn) , Holder, Martin (VerfasserIn) , Žebec, Mislav Stjepan (VerfasserIn) , Schnabel, Dirk (VerfasserIn) , Haffner, Dieter (VerfasserIn) , Zivicnjak, Miroslav (VerfasserIn)
Dokumenttyp: Article (Journal)
Sprache:Englisch
Veröffentlicht: 10 June 2025
In: Pediatric nephrology
Year: 2025, Jahrgang: 40, Heft: 10, Pages: 3187-3200
ISSN:1432-198X
DOI:10.1007/s00467-025-06841-y
Online-Zugang:Verlag, kostenfrei, Volltext: https://doi.org/10.1007/s00467-025-06841-y
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Verfasserangaben:Laura Celine Brieger, Stephan Przygodda, Alina Verena Bohlen, Mirko Rehberg, Martin Konrad, Karl Peter Schlingmann, Olaf Hiort, Dorothee Schmidt, Ulrike John-Kroegel, Elke Wuehl, Markus Josef Kemper, Ute Derichs, Ludwig Patzer, Norbert Albers, Desiree Dunstheimer, Sabine Heger, Karina Grohmann-Held, Carmen Schroeder, Norbert Jorch, Elmar Schmid, Hagen Staude, Marcus Weitz, Clemens Freiberg, Angela Huebner, Anke Heitmeyer-Pyper, Giuseppina Sparta, Carl-Joachim Partsch, Michaela Marx, Christof Land, Inka Baus, Frauke Wilkening, Kristina Moeller, Gunter Simic-Schleicher, Susann Empting, Oliver Metzing, Verena Wagner, Martin Holder, Mislav Stjepan Žebec, Dirk Schnabel, Dieter Haffner, Miroslav Zivicnjak on behalf of, the German Society for Pediatric Nephrology (GPN), the German Society for Pediatric, Diabetology (DGKED) Adolescent Endocrinology

MARC

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650 4 |a Alkaline phosphatase 
650 4 |a Body disproportion 
650 4 |a Frame index 
650 4 |a Phosphate 
650 4 |a Rickets 
650 4 |a Transversal body dimension 
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