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Supportive care for systemic amyloidosis: International Society of Amyloidosis (ISA) expert panel guidelines

Systemic amyloidosis refers to a group of protein misfolding disorders resulting in organ deposition with amyloid, leading to organ dysfunction, ultimately resulting in organ failure and death if not successfully treated. Treatment is type-specific and aimed at the underlying source of the misfolded...

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Hauptverfasser: Muchtar, Eli (VerfasserIn) , Grogan, Martha (VerfasserIn) , Siepen, Fabian aus dem (VerfasserIn) , Waddington-Cruz, Marcia (VerfasserIn) , Misumi, Yohei (VerfasserIn) , Carroll, Antonia S. (VerfasserIn) , Clarke, John O. (VerfasserIn) , Sanchorawala, Vaishali (VerfasserIn) , Milani, Paolo (VerfasserIn) , Caccialanza, Riccardo (VerfasserIn) , Da Prat, Valentina (VerfasserIn) , Pruthi, Rajiv (VerfasserIn) , Quintana, Luis F. (VerfasserIn) , Bridoux, Frank (VerfasserIn)
Dokumenttyp: Article (Journal)
Sprache:Englisch
Veröffentlicht: June 2025
In: Amyloid
Year: 2025, Jahrgang: 32, Heft: 2, Pages: 93-116
ISSN:1744-2818
DOI:10.1080/13506129.2025.2463678
Online-Zugang:Verlag, lizenzpflichtig, Volltext: https://doi.org/10.1080/13506129.2025.2463678
Volltext
Verfasserangaben:Eli Muchtar, Martha Grogan, Fabian aus dem Siepen, Marcia Waddington-Cruz, Yohei Misumi, Antonia S. Carroll, John O. Clarke, Vaishali Sanchorawala, Paolo Milani, Riccardo Caccialanza, Valentina Da Prat, Rajiv Pruthi, Luis F. Quintana and Frank Bridoux
Beschreibung
Zusammenfassung:Systemic amyloidosis refers to a group of protein misfolding disorders resulting in organ deposition with amyloid, leading to organ dysfunction, ultimately resulting in organ failure and death if not successfully treated. Treatment is type-specific and aimed at the underlying source of the misfolded protein. In the past decades, treatments have become increasingly available across the various amyloidosis types with improved response rates and longer survival. Supportive care measures are an integral part of care for patients with systemic amyloidosis to improve symptom burden and quality of life, reduce healthcare costs, and potentially prolong survival while type-directed therapy takes effect. In these guidelines, we provide supportive care recommendations across eight areas of interest in systemic amyloidosis: cardiology, nephrology, peripheral neuropathy, central nervous system involvement, autonomic neuropathy, gastroenterology, coagulopathy and bleeding, nutrition and hematology. These guidelines were developed on behalf of the International Society of Amyloidosis (ISA) by experts in the above fields and provide the best available evidence and expertise for supportive care in these rare disorders.
Beschreibung:Online veröffentlicht am 21. Februar 2025
Gesehen am 02.12.2025
Beschreibung:Online Resource
ISSN:1744-2818
DOI:10.1080/13506129.2025.2463678

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