Intestinal current measurements detect activation of mutant CFTR in patients with cystic fibrosis with the G551D mutation treated with ivacaftor

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Main Authors: Gräber, Simon Y. (Author) , Hug, Martin J. (Author) , Sommerburg, Olaf (Author) , Hirtz, Stephanie (Author) , Hentschel, Julia (Author) , Heinzmann, Andrea (Author) , Dopfer, Christian (Author) , Schulz, Angela (Author) , Mainz, Jochen G. (Author) , Tümmler, Burkhard (Author) , Mall, Marcus A. (Author)
Format: Article (Journal)
Language:English
Published: 2015
In: American journal of respiratory and critical care medicine
Year: 2015, Volume: 192, Issue: 10, Pages: 1252-1255
ISSN:1535-4970
DOI:10.1164/rccm.201507-1271LE
Online Access:Verlag, lizenzpflichtig, Volltext: https://doi.org/10.1164/rccm.201507-1271LE
Verlag, lizenzpflichtig, Volltext: https://www.atsjournals.org/doi/10.1164/rccm.201507-1271LE
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Author Notes:Simon Y. Graeber, Martin J. Hug, Olaf Sommerburg, Stephanie Hirtz, Julia Hentschel, Andrea Heinzmann, Christian Dopfer, Angela Schulz, Jochen G. Mainz, Burkhard Tümmler, and Marcus A. Mall
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Item Description:Gesehen am 14.09.2020
Physical Description:Online Resource
ISSN:1535-4970
DOI:10.1164/rccm.201507-1271LE