MPGN II - genetically determined by defective complement regulation?

MPGN II is a rare disease which is characterized by complement containing deposits within the GBM. The disease is characterized by functional impairment of the GBM causing progressive loss of renal function eventually resulting in end stage renal disease.

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Bibliographische Detailangaben
Hauptverfasser: Licht, Christoph (VerfasserIn) , Schlötzer-Schrehardt, Ursula (VerfasserIn) , Kirschfink, Michael (VerfasserIn) , Zipfel, Peter F. (VerfasserIn) , Hoppe, Bernd (VerfasserIn)
Dokumenttyp: Article (Journal)
Sprache:Englisch
Veröffentlicht: 2007
In: Pediatric nephrology
Year: 2007, Jahrgang: 22, Heft: 1, Pages: 2-9
ISSN:1432-198X
DOI:10.1007/s00467-006-0299-8
Online-Zugang:Verlag, lizenzpflichtig, Volltext: https://dx.doi.org/10.1007/s00467-006-0299-8
Verlag, lizenzpflichtig, Volltext: https://doi.org/10.1007/s00467-006-0299-8
Volltext
Verfasserangaben:Christoph Licht, Ursula Schlötzer-Schrehardt, Michael Kirschfink, Peter F. Zipfel, Bernd Hoppe
Beschreibung
Zusammenfassung:MPGN II is a rare disease which is characterized by complement containing deposits within the GBM. The disease is characterized by functional impairment of the GBM causing progressive loss of renal function eventually resulting in end stage renal disease.
Beschreibung:published online: 23 September 2006
Gesehen am 15.02.2021
Beschreibung:Online Resource
ISSN:1432-198X
DOI:10.1007/s00467-006-0299-8