Diagnosing AL and ATTR amyloid cardiomyopathy: a multidisciplinary approach

Amyloidosis with cardiac involvement is a fatal disease leading to progressive heart failure. The most common forms of amyloidosis with cardiac involvement are light chain (AL) and transthyretin (ATTR) amyloidosis. To allow effective specific treatment for both forms, precise and early diagnosis is...

Full description

Saved in:
Bibliographic Details
Main Authors: Siepen, Fabian aus dem (Author) , Hansen, Timon (Author)
Format: Article (Journal)
Language:English
Published: 1 October 2024
In: Journal of Clinical Medicine
Year: 2024, Volume: 13, Issue: 19, Pages: 1-12
ISSN:2077-0383
DOI:10.3390/jcm13195873
Online Access:Verlag, kostenfrei, Volltext: https://doi.org/10.3390/jcm13195873
Verlag, kostenfrei, Volltext: https://www.mdpi.com/2077-0383/13/19/5873
Get full text
Author Notes:Fabian aus dem Siepen and Timon Hansen
Description
Summary:Amyloidosis with cardiac involvement is a fatal disease leading to progressive heart failure. The most common forms of amyloidosis with cardiac involvement are light chain (AL) and transthyretin (ATTR) amyloidosis. To allow effective specific treatment for both forms, precise and early diagnosis is important. This review focuses on diagnostic approaches for AL and ATTR amyloidosis with cardiac involvement, including different strategies, the role of imaging and biomarkers and possible pitfalls.
Item Description:Gesehen am 27.03.2025
Physical Description:Online Resource
ISSN:2077-0383
DOI:10.3390/jcm13195873