RV-PA uncoupling is associated with increased mortality in transthyretin amyloid cardiomyopathy treated with tafamidis
The right ventricle to pulmonary artery coupling (RV-PAc) describes the right ventricle’s ability to adjust to an increased afterload. In case of transthyretin amyloid cardiomyopathy (ATTR-CM), impaired RV-PAc can result from increased left ventricular diastolic stiffness due to fibril deposition.
Saved in:
| Main Authors: | , , , , , , , , , , |
|---|---|
| Format: | Article (Journal) |
| Language: | English |
| Published: |
20 November 2024
|
| In: |
Clinical research in cardiology
|
| ISSN: | 1861-0692 |
| DOI: | 10.1007/s00392-024-02576-2 |
| Online Access: | Verlag, kostenfrei, Volltext: https://doi.org/10.1007/s00392-024-02576-2 Verlag, kostenfrei, Volltext: https://link.springer.com/article/10.1007/s00392-024-02576-2 |
| Author Notes: | Stéphanie K. Schwarting, Michael Poledniczek, Yuliyan Metodiev, Lukas Stolz, Eva Hofmann, Ute Hegenbart, Stefan Schönland, Stefan Kääb, Steffen Massberg, Norbert Frey, Fabian aus dem Siepen |
MARC
| LEADER | 00000caa a22000002c 4500 | ||
|---|---|---|---|
| 001 | 1925863301 | ||
| 003 | DE-627 | ||
| 005 | 20250717014309.0 | ||
| 007 | cr uuu---uuuuu | ||
| 008 | 250516s2024 xx |||||o 00| ||eng c | ||
| 024 | 7 | |a 10.1007/s00392-024-02576-2 |2 doi | |
| 035 | |a (DE-627)1925863301 | ||
| 035 | |a (DE-599)KXP1925863301 | ||
| 035 | |a (OCoLC)1528045436 | ||
| 040 | |a DE-627 |b ger |c DE-627 |e rda | ||
| 041 | |a eng | ||
| 084 | |a 33 |2 sdnb | ||
| 100 | 1 | |a Schwarting, Stéphanie K. |e VerfasserIn |0 (DE-588)1338320661 |0 (DE-627)189820103X |4 aut | |
| 245 | 1 | 0 | |a RV-PA uncoupling is associated with increased mortality in transthyretin amyloid cardiomyopathy treated with tafamidis |c Stéphanie K. Schwarting, Michael Poledniczek, Yuliyan Metodiev, Lukas Stolz, Eva Hofmann, Ute Hegenbart, Stefan Schönland, Stefan Kääb, Steffen Massberg, Norbert Frey, Fabian aus dem Siepen |
| 264 | 1 | |c 20 November 2024 | |
| 336 | |a Text |b txt |2 rdacontent | ||
| 337 | |a Computermedien |b c |2 rdamedia | ||
| 338 | |a Online-Ressource |b cr |2 rdacarrier | ||
| 500 | |a Gesehen am 16.05.2025 | ||
| 520 | |a The right ventricle to pulmonary artery coupling (RV-PAc) describes the right ventricle’s ability to adjust to an increased afterload. In case of transthyretin amyloid cardiomyopathy (ATTR-CM), impaired RV-PAc can result from increased left ventricular diastolic stiffness due to fibril deposition. | ||
| 650 | 4 | |a Acute Heart Failure | |
| 650 | 4 | |a Amyloidosis | |
| 650 | 4 | |a Arterial stiffening | |
| 650 | 4 | |a Echocardiography | |
| 650 | 4 | |a Heart failure | |
| 650 | 4 | |a Idiopathic thrombocytopaenic purpura | |
| 650 | 4 | |a Retinopathy of prematurity | |
| 650 | 4 | |a RV-PA coupling | |
| 650 | 4 | |a TAPSE/PASP-ratio | |
| 650 | 4 | |a Transthyretin | |
| 650 | 4 | |a Valvular disease | |
| 700 | 1 | |a Poledniczek, Michael |e VerfasserIn |4 aut | |
| 700 | 1 | |a Metodiev, Yuliyan |e VerfasserIn |4 aut | |
| 700 | 1 | |a Stolz, Lukas |d 1996- |e VerfasserIn |0 (DE-588)1278903615 |0 (DE-627)1831802236 |4 aut | |
| 700 | 1 | |a Hofmann, Eva Catarina Maria |d 1990- |e VerfasserIn |0 (DE-588)1151084603 |0 (DE-627)1011280558 |0 (DE-576)49748272X |4 aut | |
| 700 | 1 | |a Hegenbart, Ute |e VerfasserIn |0 (DE-588)1028373708 |0 (DE-627)73062157X |0 (DE-576)35901903X |4 aut | |
| 700 | 1 | |a Schönland, Stefan |d 1969- |e VerfasserIn |0 (DE-588)122405226 |0 (DE-627)705896137 |0 (DE-576)293255792 |4 aut | |
| 700 | 1 | |a Kääb, Stefan |e VerfasserIn |4 aut | |
| 700 | 1 | |a Maßberg, Steffen |d 1970- |e VerfasserIn |0 (DE-588)118136399 |0 (DE-627)694702501 |0 (DE-576)29173409X |4 aut | |
| 700 | 1 | |a Frey, Norbert |e VerfasserIn |0 (DE-588)141244976 |0 (DE-627)625824075 |0 (DE-576)322969514 |4 aut | |
| 700 | 1 | |a Siepen, Fabian aus dem |d 1984- |e VerfasserIn |0 (DE-588)1066499969 |0 (DE-627)817646469 |0 (DE-576)426014944 |4 aut | |
| 773 | 0 | 8 | |i Enthalten in |t Clinical research in cardiology |d Berlin : Springer, 2006 |g (2024) |h Online-Ressource |w (DE-627)506287343 |w (DE-600)2218331-0 |w (DE-576)251097692 |x 1861-0692 |7 nnas |a RV-PA uncoupling is associated with increased mortality in transthyretin amyloid cardiomyopathy treated with tafamidis |
| 773 | 1 | 8 | |g year:2024 |a RV-PA uncoupling is associated with increased mortality in transthyretin amyloid cardiomyopathy treated with tafamidis |
| 856 | 4 | 0 | |u https://doi.org/10.1007/s00392-024-02576-2 |x Verlag |x Resolving-System |z kostenfrei |3 Volltext |
| 856 | 4 | 0 | |u https://link.springer.com/article/10.1007/s00392-024-02576-2 |x Verlag |z kostenfrei |3 Volltext |
| 951 | |a AR | ||
| 992 | |a 20250516 | ||
| 993 | |a Article | ||
| 994 | |a 2024 | ||
| 998 | |g 1066499969 |a Siepen, Fabian aus dem |m 1066499969:Siepen, Fabian aus dem |d 910000 |d 910100 |e 910000PS1066499969 |e 910100PS1066499969 |k 0/910000/ |k 1/910000/910100/ |p 11 | ||
| 998 | |g 141244976 |a Frey, Norbert |m 141244976:Frey, Norbert |d 910000 |d 910100 |e 910000PF141244976 |e 910100PF141244976 |k 0/910000/ |k 1/910000/910100/ |p 10 | ||
| 998 | |g 122405226 |a Schönland, Stefan |m 122405226:Schönland, Stefan |d 910000 |d 910100 |d 50000 |e 910000PS122405226 |e 910100PS122405226 |e 50000PS122405226 |k 0/910000/ |k 1/910000/910100/ |k 0/50000/ |p 7 | ||
| 998 | |g 1028373708 |a Hegenbart, Ute |m 1028373708:Hegenbart, Ute |d 910000 |d 910100 |d 50000 |e 910000PH1028373708 |e 910100PH1028373708 |e 50000PH1028373708 |k 0/910000/ |k 1/910000/910100/ |k 0/50000/ |p 6 | ||
| 998 | |g 1151084603 |a Hofmann, Eva Catarina Maria |m 1151084603:Hofmann, Eva Catarina Maria |d 910000 |d 910100 |e 910000PH1151084603 |e 910100PH1151084603 |k 0/910000/ |k 1/910000/910100/ |p 5 | ||
| 998 | |g 1338320661 |a Schwarting, Stéphanie K. |m 1338320661:Schwarting, Stéphanie K. |d 910000 |d 910100 |e 910000PS1338320661 |e 910100PS1338320661 |k 0/910000/ |k 1/910000/910100/ |p 1 |x j | ||
| 999 | |a KXP-PPN1925863301 |e 4725175358 | ||
| BIB | |a Y | ||
| SER | |a journal | ||
| JSO | |a {"id":{"eki":["1925863301"],"doi":["10.1007/s00392-024-02576-2"]},"title":[{"title":"RV-PA uncoupling is associated with increased mortality in transthyretin amyloid cardiomyopathy treated with tafamidis","title_sort":"RV-PA uncoupling is associated with increased mortality in transthyretin amyloid cardiomyopathy treated with tafamidis"}],"recId":"1925863301","note":["Gesehen am 16.05.2025"],"language":["eng"],"type":{"bibl":"article-journal","media":"Online-Ressource"},"origin":[{"dateIssuedDisp":"20 November 2024","dateIssuedKey":"2024"}],"name":{"displayForm":["Stéphanie K. Schwarting, Michael Poledniczek, Yuliyan Metodiev, Lukas Stolz, Eva Hofmann, Ute Hegenbart, Stefan Schönland, Stefan Kääb, Steffen Massberg, Norbert Frey, Fabian aus dem Siepen"]},"person":[{"family":"Schwarting","roleDisplay":"VerfasserIn","display":"Schwarting, Stéphanie K.","role":"aut","given":"Stéphanie K."},{"family":"Poledniczek","roleDisplay":"VerfasserIn","given":"Michael","display":"Poledniczek, Michael","role":"aut"},{"display":"Metodiev, Yuliyan","role":"aut","given":"Yuliyan","family":"Metodiev","roleDisplay":"VerfasserIn"},{"family":"Stolz","roleDisplay":"VerfasserIn","given":"Lukas","role":"aut","display":"Stolz, Lukas"},{"role":"aut","display":"Hofmann, Eva Catarina Maria","given":"Eva Catarina Maria","family":"Hofmann","roleDisplay":"VerfasserIn"},{"family":"Hegenbart","roleDisplay":"VerfasserIn","given":"Ute","display":"Hegenbart, Ute","role":"aut"},{"given":"Stefan","display":"Schönland, Stefan","role":"aut","family":"Schönland","roleDisplay":"VerfasserIn"},{"given":"Stefan","display":"Kääb, Stefan","role":"aut","family":"Kääb","roleDisplay":"VerfasserIn"},{"role":"aut","display":"Maßberg, Steffen","given":"Steffen","roleDisplay":"VerfasserIn","family":"Maßberg"},{"display":"Frey, Norbert","role":"aut","given":"Norbert","roleDisplay":"VerfasserIn","family":"Frey"},{"given":"Fabian aus dem","role":"aut","display":"Siepen, Fabian aus dem","family":"Siepen","roleDisplay":"VerfasserIn"}],"relHost":[{"physDesc":[{"extent":"Online-Ressource"}],"part":{"text":"(2024)","year":"2024"},"type":{"bibl":"periodical","media":"Online-Ressource"},"origin":[{"publisher":"Springer","dateIssuedDisp":"2006-","dateIssuedKey":"2006","publisherPlace":"Berlin"}],"language":["eng"],"pubHistory":["95.2006 -"],"recId":"506287343","id":{"zdb":["2218331-0"],"eki":["506287343"],"issn":["1861-0692"]},"title":[{"title":"Clinical research in cardiology","title_sort":"Clinical research in cardiology"}],"disp":"RV-PA uncoupling is associated with increased mortality in transthyretin amyloid cardiomyopathy treated with tafamidisClinical research in cardiology"}]} | ||
| SRT | |a SCHWARTINGRVPAUNCOUP2020 | ||