Pulmonary lymphangiomatosis: insights into an ultra-rare disease

Pulmonary lymphangiomatosis (PL) is an ultrarare disease characterized by diffuse infiltration of the lung, pleura and/or mediastinum by abnormal lymphatic proliferation. Consented diagnostic or treatment approaches are not established. We therefore aimed to collect data on diagnostics and treatment...

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Main Authors: Polke, Markus (Author) , Polke, N. (Author) , Piel, Stella (Author) , Brunnemer, Eva (Author) , Wälscher, J. (Author) , Buschulte, Katharina (Author) , Warth, Arne (Author) , Heußel, Claus Peter (Author) , Eichinger, Monika (Author) , Frankenstein, Lutz (Author) , Eichhorn, Martin E. (Author) , Miliauskas, S. (Author) , Herth, Felix (Author) , Kreuter, M. (Author)
Format: Article (Journal)
Language:English
Published: 26 November 2024
In: Respiratory research
Year: 2024, Volume: 25, Pages: 1-10
ISSN:1465-993X
DOI:10.1186/s12931-024-03040-5
Online Access:Verlag, kostenfrei, Volltext: https://doi.org/10.1186/s12931-024-03040-5
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Author Notes:M. Polke, N. Polke, S. Piel, E. Brunnemer, J. Wälscher, K. Buschulte, A. Warth, C.P. Heussel, M. Eichinger, L. Frankenstein, M. Eichhorn, S. Miliauskas, F.J.F. Herth and M. Kreuter
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Summary:Pulmonary lymphangiomatosis (PL) is an ultrarare disease characterized by diffuse infiltration of the lung, pleura and/or mediastinum by abnormal lymphatic proliferation. Consented diagnostic or treatment approaches are not established. We therefore aimed to collect data on diagnostics and treatments in a cohort of patients with PL from a tertiary center for rare lung diseases.
Item Description:Gesehen am 01.07.2025
Physical Description:Online Resource
ISSN:1465-993X
DOI:10.1186/s12931-024-03040-5