Pulmonary lymphangiomatosis: insights into an ultra-rare disease
Pulmonary lymphangiomatosis (PL) is an ultrarare disease characterized by diffuse infiltration of the lung, pleura and/or mediastinum by abnormal lymphatic proliferation. Consented diagnostic or treatment approaches are not established. We therefore aimed to collect data on diagnostics and treatment...
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| Main Authors: | , , , , , , , , , , , , , |
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| Format: | Article (Journal) |
| Language: | English |
| Published: |
26 November 2024
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| In: |
Respiratory research
Year: 2024, Volume: 25, Pages: 1-10 |
| ISSN: | 1465-993X |
| DOI: | 10.1186/s12931-024-03040-5 |
| Online Access: | Verlag, kostenfrei, Volltext: https://doi.org/10.1186/s12931-024-03040-5
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| Author Notes: | M. Polke, N. Polke, S. Piel, E. Brunnemer, J. Wälscher, K. Buschulte, A. Warth, C.P. Heussel, M. Eichinger, L. Frankenstein, M. Eichhorn, S. Miliauskas, F.J.F. Herth and M. Kreuter |
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| 520 | |a Pulmonary lymphangiomatosis (PL) is an ultrarare disease characterized by diffuse infiltration of the lung, pleura and/or mediastinum by abnormal lymphatic proliferation. Consented diagnostic or treatment approaches are not established. We therefore aimed to collect data on diagnostics and treatments in a cohort of patients with PL from a tertiary center for rare lung diseases. | ||
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