Progression of QRS duration: a potential surrogate marker of survival in ATTRwt amyloidosis patients

In wild-type transthyretin amyloidosis (ATTRwt), the deposition of transthyretin in the myocardium leads to progressive heart failure. However, little is known about the short-term natural progression of this disease and potential predictors of outcome.

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Bibliographische Detailangaben
Hauptverfasser: Hein, Selina (VerfasserIn) , Siepen, Fabian aus dem (VerfasserIn) , Zierleyn, Sonja M. (VerfasserIn) , Knoll, Maximilian (VerfasserIn) , Katus, Hugo (VerfasserIn) , Frey, Norbert (VerfasserIn) , Kristen, Arnt (VerfasserIn)
Dokumenttyp: Article (Journal)
Sprache:Englisch
Veröffentlicht: 20 October 2025
In: Orphanet journal of rare diseases
Year: 2025, Jahrgang: 20, Heft: 1, Pages: 1-9
ISSN:1750-1172
DOI:10.1186/s13023-025-04078-4
Online-Zugang:Resolving-System, kostenfrei, Volltext: https://doi.org/10.1186/s13023-025-04078-4
Verlag, kostenfrei, Volltext: https://link.springer.com/article/10.1186/s13023-025-04078-4
Volltext
Verfasserangaben:Selina Hein, Fabian aus dem Siepen, Sonja M. Zierleyn, Maximilian Knoll, Hugo A. Katus, Norbert Frey, Arnt V. Kristen

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