Cover Image

Timing of renal replacement therapy does not influence survival and growth in children with congenital nephrotic syndrome caused by mutations in NPHS1: data from the ESPN/ERA-EDTA Registry

Congenital nephrotic syndrome (CNS) of the Finnish type, NPHS1, is the most severe form of CNS. Outcomes of renal replacement therapy (RRT) in NPHS1 patients in Europe were analysed using data from the ESPN/ERA-EDTA Registry. As NPHS1 is most prevalent in Finland and the therapeutic approach differs...

Full description

Saved in:
Bibliographic Details
Main Authors: Hölttä, Tuula (Author) , Bonthuis, Marjolein (Author) , Van Stralen, Karlijn J. (Author) , Bjerre, Anna (Author) , Topaloglu, Rezan (Author) , Ozaltin, Fatih (Author) , Holmberg, Christer (Author) , Harambat, Jerome (Author) , Jager, Kitty J. (Author) , Schaefer, Franz (Author) , Groothoff, Jaap W. (Author)
Format: Article (Journal)
Language:English
Published: 20 October 2016
In: Pediatric nephrology
Year: 2016, Volume: 31, Issue: 12, Pages: 2317-2325
ISSN:1432-198X
DOI:10.1007/s00467-016-3517-z
Online Access:Verlag, lizenzpflichtig, Volltext: https://doi.org/10.1007/s00467-016-3517-z
Get full text
Author Notes:Tuula Hölttä, Marjolein Bonthuis, Karlijn J. Van Stralen, Anna Bjerre, Rezan Topaloglu, Fatih Ozaltin, Christer Holmberg, Jerome Harambat, Kitty J. Jager, Franz Schaefer, Jaap W. Groothoff
Description
Summary:Congenital nephrotic syndrome (CNS) of the Finnish type, NPHS1, is the most severe form of CNS. Outcomes of renal replacement therapy (RRT) in NPHS1 patients in Europe were analysed using data from the ESPN/ERA-EDTA Registry. As NPHS1 is most prevalent in Finland and the therapeutic approach differs from that in many other countries, we compared outcomes in Finnish and other European patients.
Item Description:Gesehen am 20.05.2020
Physical Description:Online Resource
ISSN:1432-198X
DOI:10.1007/s00467-016-3517-z

Similar Items