Evaluation of right ventricular function in patients with propionic acidemia: a cross-sectional study

In propionic acidemia (PA), myocardial involvement often leads to progressive cardiac dysfunction of the left ventricle (LV). Cardiomyopathy (CM) is an important contributor to mortality. Although known to be of prognostic value in CM, there are no published data on right ventricular (RV) function i...

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Main Authors: Kovacevic, Alexander (Author) , Garbade, Sven (Author) , Hörster, Friederike (Author) , Hoffmann, Georg F. (Author) , Gorenflo, Matthias (Author) , Mereles, Derliz (Author) , Kölker, Stefan (Author) , Staufner, Christian (Author)
Format: Article (Journal)
Language:English
Published: 5 January 2023
In: Children
Year: 2023, Volume: 10, Issue: 1, Pages: 1-13
ISSN:2227-9067
DOI:10.3390/children10010113
Online Access:Verlag, kostenfrei, Volltext: https://doi.org/10.3390/children10010113
Verlag, kostenfrei, Volltext: https://www.mdpi.com/2227-9067/10/1/113
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Author Notes:Alexander Kovacevic, Sven F. Garbade, Friederike Hörster, Georg F. Hoffmann, Matthias Gorenflo, Derliz Mereles, Stefan Kölker and Christian Staufner
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Summary:In propionic acidemia (PA), myocardial involvement often leads to progressive cardiac dysfunction of the left ventricle (LV). Cardiomyopathy (CM) is an important contributor to mortality. Although known to be of prognostic value in CM, there are no published data on right ventricular (RV) function in PA patients.
Item Description:Gesehen am 14.11.2023
Physical Description:Online Resource
ISSN:2227-9067
DOI:10.3390/children10010113